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Volume 5, Issue 1, June 2021, Page: 1-3
Supratentorial Hemangioblastomas Without Von - Hippel Lindau Disease – Case Report and Review
Jose Carlos Rodrigues Junior, Department of Neurosurgery, Heliópolis Hospital, São Paulo, Brazil; Department of Neurosurgery, Assunção Hospital, São Paulo, Brazil
Vithor Ely Bortholin da Silva, Department of Neurosurgery, Heliópolis Hospital, São Paulo, Brazil
Roberto Bezerra Vital, Department of Neurosurgery, Assunção Hospital, São Paulo, Brazil
Renan Luiz Lapate, Department of Neurosurgery, Assunção Hospital, São Paulo, Brazil
Marcelo Ferraz Campos, Department of Neurosurgery, Heliópolis Hospital, São Paulo, Brazil
Received: Apr. 27, 2020;       Accepted: Aug. 19, 2020;       Published: Jan. 4, 2021
DOI: 10.11648/j.ijn.20210501.11      View  20      Downloads  11
Abstract
Background and Importance: Hemangioblastomas (HBL) are tumors constantly present in the neurosurgeon's daily life, affecting mainly the posterior fossa region. In patients with von Hippel-Lindau, their presence is even more striking. However, the authors, through a report of a case with the literature review, show that hemangioblastomas should also be part of the range of differential diagnoses of supratentorial lesions even in patients not carrying the genetic mutation. Clinical Presentation: A 45-year-old male patient has a 2 weeks history of headache associated with nauseas and vertigo. In the last two weeks the pain was being progressively more frequently with increase in intensity and duration. At examination he was oriented, with face of pain, muscle examination was normal as all the neurological examination. The patient was submitted to a Magnetic Resonance (MR) of the brain that showed an expansive lesion in the brain located in the left frontal lobe, adjacent to the medial line with moderated adjacent edema and with gadolinium injection the tumor was heterogeneous almost solid with cystic parts and including adjacent impregnation of the dura of the midline. Surgical treatment was done. The lesion was completed resected including the dura of the convexity that was invaded by the tumor. Postoperative period was uneventful, with resolution of the headache and no deficits. Patient was discharged 3 days after surgery. Pathology reveals the lesion was a hemangioblastoma. Patient made genetic exams and confirms that didn’t have Von Hippel Lindau disease. MR of the brain, almost 3 years of the surgery, reveals no tumor. Conclusion: Hemangioblastoma is a rare tumor, especially in its supratentorial location. However, this case reflects the importance of including HBL as a differential diagnostic allowing a better therapeutic planning, ensuring better prognosis and facilitating their treatment.
Keywords
Hemangioblastoma, Supratentorial, Von Hippel Lindau, Brain Tumor
To cite this article
Jose Carlos Rodrigues Junior, Vithor Ely Bortholin da Silva, Roberto Bezerra Vital, Renan Luiz Lapate, Marcelo Ferraz Campos, Supratentorial Hemangioblastomas Without Von - Hippel Lindau Disease – Case Report and Review, International Journal of Neurosurgery. Vol. 5, No. 1, 2021, pp. 1-3. doi: 10.11648/j.ijn.20210501.11
Copyright
Copyright © 2021 Authors retain the copyright of this article.
This article is an open access article distributed under the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0/) which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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